Naslov: | Henoch-Schönleinova purpura pri odraslem |
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Avtorji: | ID Skačej, Helena (Avtor) ID Holc, Iztok (Avtor) ID Pahor, Artur (Avtor) |
Datoteke: | 09.pdf (231,67 KB) MD5: BB60BA7BC8277B8521BD8ADC4C0D21A7
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Jezik: | Angleški jezik |
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Vrsta gradiva: | Znanstveno delo |
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Tipologija: | 1.01 - Izvirni znanstveni članek |
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Organizacija: | MF - Medicinska fakulteta
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Opis: | Background: Henoch-Schonlein purpura (HSP) is a systemic inflammation of small-vessel walls that predominantly affects children. In adults, on the other hand, it appears rarely, and can be more severe. The disease is characterised by a tetrad of clinical signs which manifest the skin, joint, gastrointestinal, and kidney involvement. HSP is diagnosed using internationally-accepted criteria. At present, there is no effective specific therapy for children and adults. However, in cases of severe organ involvement, aggressive treatment may stabilise the disease. Case report: We present a case of a 59-year-old immunologically uncom- promised patient with an extremely severe form of HSP. Epidemiology, etiopathogenesis, clinical features, diagnostic procedures, differential diagnosis, treatment, and prognosis of the disease are discussed. Conclusions: The patient was treated with corticosteroids, human polyspecific immunoglobulins, and immunosuppressive agents. A satisfactory clinical remission has been achieved. |
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Ključne besede: | sistemski vaskulitis, Henoch-Schönleinova purpura, odrasli bolnik |
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Status publikacije: | Objavljeno |
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Verzija publikacije: | Objavljena publikacija |
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Datum objave: | 01.01.2009 |
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Leto izida: | 2009 |
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Št. strani: | str. 61-68 |
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Številčenje: | Vol. 2, no. 2 |
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PID: | 20.500.12556/DKUM-88381  |
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UDK: | 616.1-002 |
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COBISS.SI-ID: | 3494975  |
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ISSN pri članku: | 1855-5640 |
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Datum objave v DKUM: | 19.04.2024 |
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Število ogledov: | 184 |
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Število prenosov: | 3 |
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Metapodatki: |  |
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Področja: | Ostalo
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